Home
Index
Search
Links
Pathology
Molecules
Syndromes
  Muscle
NMJ
Nerve
Spinal
Ataxia
Antibody & Biopsy
Patient Information


IMAGES

Figure index
  Pathology
  Illustrations

Differential diagnosis
  Muscle biopsy
  Nerve biopsy
  NMJ

General
  Muscle biopsy
    Stains
  Nerve biopsy

Myotendinous Junction

Perlecan at a Myotendinous Junction




Pathology

Myopathy: Inflammatory & Immune
  Brachio-Cervical
  Chondroitin sulfate C, Deficient
  Complement deposition
  Decorin (BJ) antibody
  Dermatomyositis
    Childhood pattern
    Variant adult pattern
  Fasciitis
  Focal myositis
  Granulomas
  Hemophagocytic lymphohistiocytosis
  IMPP
  Inclusion Body Myositis
  Inflammation: Muscle
  Inflammation: Cell patterns
  Jo-1 Myositis
  MHC-1
  Macrophages, abundant (IMAM)
  Macrophagic myofasciitis
  Mitochondrial dysfunction
  Necrosis: Muscle fibers
  Neonatal perifascicular
  Nodular myositis
  Paraneoplastic necrotic
  Perimysial pathology
  Pipestem capillaries
  Scleromyxedema
  Signal recognition particle
  Trichinosis: Acute; Chronic
  Vasculitis: Small & Large vessel

Myopathy: Other
  Atrophy: Type I; Type 2
  CADASIL: Vessels
  Calciphylaxis
  Colchicine
  Cytoplasmic bodies
  Hemosiderin
  Internal architecture: NADH
  Lymphoma, Intravascular
  Mitochondrial
    Cytochrome oxidase deficiency
    Megaconial
    MELAS
    Ultrastructure
  Myosin-loss myopathy
  Posterior neck
  Ring fibers
  Tubular aggregates

Muscle
  Exercise changes
  Unknowns

Muscle: Storage
  Amyloid
    Pathology; Birefringence
  CADASIL
  Carbohydrate
    Acid Maltase Deficiency
      Child & Adult
    Phosphorylase deficiency
    Also see: Pathways
  Lipid
  Lipofuscin
  Myofibrillar (Desmin-storage)

Myopathy: Congenital
  Cap
  Central core
  Centronuclear (Myotubular)
  Congenital muscular dystrophy
  Fiber type size disproportion
    Fiber type disorders
    Type I small
    Type II small
  Fukuyama
  Marinesco-Sjögren
  Multicore
  Nemaline rod myopathy
  Reducing body
  Ullrich CMD

Myopathy: Hereditary
  Autophagy
  Becker MD
  Danon disease
  Distal myopathy: Vacuolar
  Duchenne MD
  Dystrophin & related proteins
  Emery-Dreifuss MD
  FKRP
  FSH Dystrophy
  Hereditary IBM 2
  IBM, Paget's & Dementia
  LGMD 1A
  LGMD 2A
  LGMD 2B
  LGMD 2C
  LGMD 2D
  Myotonic: DM1; DM2
  Oculopharyngeal
  Periodic paralysis, Hypokalemic

Myelin
  CIDP
    Childhood
  Demyelination: Chronic
  Dysmyelination
  Proteins
Neuromuscular junction
  Anti-AChR antibody actions
  Distal motor axons
  Normal
  Myasthenia Gravis
  Terminal axons
  Presynaptic
  Postsynaptic

Neuropathy & Neuronopathy
  Amyloid
  Angiotropic Lymphoma
  Antibody-related
    MAG
    TS-HDS
  Axonal loss
    Bungner bands
    Large fiber
  Axonal swellings
    Giant axonal neuropathy
    Polygucosan bodies
  Botulism
  Demyelination
    Active
    Chronic
    Tomaculae
  Denervation of muscle
    ALS
    Chronic denervation
      Inactive: Fiber type grouping
      Partial: Large grouped atrophy
      Partial: Ongoing
    Spinal muscular atrophy
        Bulbospinal
        SMA 5q
    Target fibers
  Differential fascicular loss
  Dysmyelination
  Minifascicles
  Nerve: Normal
    Neurofilament stain
  Perineuritis
  Regeneration
  Subperineurial edema
  Tabes dorsalis
  Terminal sprouting
  Vasculitis
  Vasculopathy
    Vessel: Thick wall
  Wallerian degeneration

Credits
  Histochemical stains performed by Jim Planer or Ruma Banerjee
  Immunocytochemical stains performed by Jin Yue, Shobna Mehta or Rati Choksi


Illustrations

Cell constituents & Pathways
  Acetylcholine receptors
  Botulinum toxin
  Dystrophin & DAGs
  Fatty acid transport
  Glycogen & Glucose metabolism
  Glycolipids
  Ion channels
    Ca++; Na+; K+
  Lysosomal pathway
  Mitochondrial
  Motor neuron
  Myelin
    Proteins
    Structure
      Cross-section
      Longitudinal
  Myogenesis
  Neuromuscular junction
  Spliceosome
    Function & Mechanism
  Tendon reflex arcs
  Ubiquitin-Proteasome Pathway
  Vitamins

Muscle fiber
  Excitation-Contraction Coupling
  Myosin & related proteins
  Structure & contraction

Autonomic
  Pathways

Cranial nerve anatomy
  Visual fields
  3, 4, 5, 6, 7, 8, 9, 10, 11, 12

Antibodies
  ANA patterns
  Anti-neural (cerebellum)
Electrophysiology
  Complex repetitive discharges
  Conduction Block: Motor
  Denervation of muscle
    Partial
    Fibrillations
    Motor unit: Rapid firing
  Demyelinating neuropathy
  Myasthenia gravis
  Myasthenic syndrome
  Myokymia
  Myopathy
  Myotonia
  Palmaris brevis spasm
  Positive sharp waves
  Prolonged distal latency
  Pseudofacilitation
  Repetitive response to 1 stimulus
  Stiffman syndrome
  Temporal dispersion
  Tetany

MRI & Imaging
  ALS
  AVM
  Bent spine syndrome
  Calcinosis
  CMT-X1
  Corpus callosum: Thin
  Dystrophinopathy: Female carrier
  Focal myositis
  Hematoma (Psoas)
  HIBM2
  Heroin myelopathy
  Myopathies
  Nephrogenic fibrosis
  Posterior neck myopathy
  Superficial siderosis
  Syringomyelia
  Thymoma
Patient pictures
  Acromegaly
  Addison's disease
  Aging
  ALS: MRI; Tongue
  Ankylosing spondylitis
  Becker dystrophy: Legs
  Bethlem myopathy: Hands
  Bulbo-Spinal Muscular Atrophy
  Calcinosis
  Cleidocranial dysplasia
  CMT-X1
  Congenital muscular dystrophy
  Congenital myasthenia gravis
  Duchenne MD
  FSH dystrophy
  Giant axonal neuropathy
  Hereditary sensory neuropathy
  HIBM + Dementia & Pagets
  King-Denborough Syndrome
  Muscle wasting
  Myasthenia gravis
  Myxedema
  Myositis
    Dermatomyositis: Hands; Rash
    Inclusion body myositis
    Pyomyositis (MRI)
  Polio
  SMA 5q: A; B

Disease pathophysiology
  DNA: CTG repeats
  DM1 locus
  FSH DNA
  Myasthenia gravis



Return to Neuromuscular Home Page
Return to Muscle biopsy
Return to Nerve biopsy

12/13/2011