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IMAGES

Figure index
  Pathology
  Illustrations

Differential diagnosis
  Muscle biopsy
  Nerve biopsy
  NMJ

General
  Muscle biopsy
    Stains
  Nerve biopsy

Myotendinous Junction

Perlecan at a Myotendinous Junction



Pathology images: Muscle & Nerve

Myopathy: Hereditary
  Congenital
  Cap
  Central core
  Centronuclear (Myotubular)
  Congenital MD
    Lamin A/C
    Laminin-α2
  Fiber type disorders
    Type I small
    Type II small
  Fukuyama
  Marinesco-Sjögren
  Multicore
  Nemaline rod myopathy
  Reducing body
  Ullrich CMD

  Storage
  Amyloid
    Pathology
    Birefringence
  CADASIL
  Carbohydrate
    Acid Maltase
      Child
      Adult
    Phosphorylase
  Lipid
  Lipofuscin
  Myofibrillar (Desmin)
  Dystrophy+
  Autophagy
  AVSF
  Becker MD
  Cytoplasmic bodies
  Danon disease
  Duchenne MD
  Emery-Dreifuss MD
  FKRP
  FSH Dystrophy
  IBM, Paget, FTD
  LGMD 1A
  LGMD 2A
  LGMD 2B
  LGMD 2C
  LGMD 2D
  Mitochondrial
    COX deficient
    Megaconial
    MELAS
    Ultrastructure
  Myotonic
    DM1
    DM2
  Oculopharyngeal
  Periodic paralysis
    Hypokalemic
  Tubular aggregates
  Vacuolar
    IBM 2
    Distal myopathy
Myopathy +
Inflammatory & Immune  
  Brachio-Cervical
  Chondroitin sulfate C Δ
  Complement deposition
  Decorin (BJ) antibody
  Dermatomyositis
    Childhood pattern
    Adult-onset IMPP
  Fasciitis
  Focal myositis
  Granulomas
  Hemophagocytic
      lymphohistiocytosis

  HMGCR antibody
  IMPP
  Inclusion Body Myositis
  Inflammation: Muscle
  Inflammation: Cell patterns
  Jo-1 IMPP
  MHC-1
  Macrophages, abundant
  Macrophagic myofasciitis
  Mitochondrial dysfunction
  Necrosis: Muscle fibers
  Neonatal perifascicular
  Nodular myositis
  Paraneoplastic necrotic
  Perimysial pathology
  Pipestem capillaries
  PL-12 IMPP
  Scleromyxedema
  Signal recognition particle
  TRAPs
  Trichinosis
    Acute
    Chronic
Myopathy: Other
  Calciphylaxis
  Colchicine
  Hemosiderin
  Internal architecture
  Lymphoma, IV
  Myosin-loss
  Posterior neck
  Ring fibers

Muscle
  Exercise changes
  Unknowns

NMJ
  Distal motor axons
  Normal
  Myasthenia Gravis
  Terminal axons
  Presynaptic
  Postsynaptic
Neuropathy & Neuronopathy
  Amyloid
  Angiotropic Lymphoma
  Antibody-related
    MAG
    TS-HDS
  Axonal loss
    Bungner bands
    Large fiber
  Axonal swellings
    Giant axonal neuropathy
    Polygucosan bodies
  Botulism
  CADASIL: Vessels
  Denervation of muscle
    ALS
    Chronic denervation
      Fiber type groups
      Grouped atrophy
      Ongoing
    Spinal muscular atrophy
        Bulbospinal
        SMA 5q
        SMA-LED
    Target fibers
  Differential fascicular loss
  DMAPN
  Dysmyelination
  Minifascicles
  Myelin & Pathology
    CIDP
      Childhood
    Demyelination
      Active
      Chronic
    Dysmyelination
    HNPP
    Proteins
    Tomaculae
  Nerve: Normal
    Neurofilament stain
  Neuroma
  Perineuritis
  Regeneration
  Subperineurial edema
  Tabes dorsalis
  Terminal sprouting
  Vasculitis
  Vasculopathy, immune
    Vessel: Thick wall
    Small vessel
    Large vessel
  Wallerian degeneration

Credits
  Histochemical stains performed by Jim Planer or Ruma Banerjee
  Immunocytochemical stains performed by Jin Yue, Shobna Mehta or Rati Choksi


Illustrations

Cell constituents & Pathways
  Acetylcholine receptors
    AChR antibody actions
  Botulinum toxin
  Dystrophin & DAGs
  Fatty acid transport
  Glycogen & Glucose metabolism
  Glycolipids
  Ion channels
    Ca++; Na+; K+
  Lysosomal pathway
  Mitochondrial
  Motor neuron
  Myelin
    Proteins
    Structure
      Cross-section
      Longitudinal
  Myogenesis
  Neuromuscular junction
  Spliceosome
    Function & Mechanism
  Tendon reflex arcs
  Ubiquitin-Proteasome Pathway
  Vitamins

Muscle fiber
  Excitation-Contraction Coupling
  Myosin & related proteins
  Structure & contraction

Autonomic
  Pathways

Cranial nerve anatomy
  Visual fields
  3, 4, 5, 6, 7, 8, 9, 10, 11, 12

Antibodies
  ANA patterns
  Anti-neural (cerebellum)
Electrophysiology
  Complex repetitive discharges
  Conduction Block: Motor
  Denervation of muscle
    Partial
    Fibrillations
    Motor unit: Rapid firing
  Demyelinating neuropathy
  Myasthenia gravis
  Myasthenic syndrome
  Myokymia
  Myopathy
  Myotonia
  Palmaris brevis spasm
  Positive sharp waves
  Prolonged distal latency
  Pseudofacilitation
  Repetitive response to 1 stimulus
  Stiffman syndrome
  Temporal dispersion
  Tetany

MRI & Imaging
  ALS
  AVM
  Bent spine syndrome
  Calcinosis
  CMT-X1
  Corpus callosum: Thin
  Dystrophinopathy: Female carrier
  Focal myositis
  Hematoma (Psoas)
  HIBM2
  Heroin myelopathy
  Myopathies
  Nephrogenic fibrosis
  Posterior neck myopathy
  Superficial siderosis
  Syringomyelia
  Thymoma
Patient pictures
  Acromegaly
  Addison's disease
  Aging
  ALS: MRI; Tongue
  Ankylosing spondylitis
  Becker dystrophy: Legs
  Bethlem myopathy: Hands
  Bulbo-Spinal Muscular Atrophy
  Calcinosis
  Cleidocranial dysplasia
  CMT-X1
  Congenital muscular dystrophy
  Congenital myasthenia gravis
  Duchenne MD
  FSH dystrophy
  Giant axonal neuropathy
  Hereditary sensory neuropathy
  HIBM + Dementia & Pagets
  King-Denborough Syndrome
  Muscle wasting
  Myasthenia gravis
  Myxedema
  Myositis
    Dermatomyositis: Hands; Rash
    Inclusion body myositis
    Pyomyositis (MRI)
  Polio
  SMA 5q: A; B

Disease pathophysiology
  DNA: CTG repeats
  DM1 locus
  FSH DNA
  Myasthenia gravis



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5/22/2013