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IMAGES

Figure index
  Pathology
  Illustrations

Differential diagnosis
  Muscle biopsy
  Nerve biopsy
  NMJ

General
  Muscle biopsy
    Stains
  Nerve biopsy

Myotendinous Junction

Perlecan at a Myotendinous Junction




Pathology

Myopathy: Inflammatory & Immune
  Absent chondroitin sulfate C
  Anti-Decorin (BJ) antibody
  Brachio-Cervical
  Complement deposition
  Decorin
  Dermatomyositis
    Childhood pattern
    Variant adult pattern
  Fasciitis
  Focal myositis
  Granulomas
  Hemophagocytic lymphohistiocytosis
  IMPP
  Inclusion Body Myositis
  Inflammation: Muscle
  Inflammation: Cell patterns
  Jo-1 Myositis
  MHC-1
  Macrophages, abundant (IMAM)
  Macrophagic myofasciitis
  Mitochondrial dysfunction
  Necrosis: Muscle fibers
  Neonatal perifascicular
  Nodular myositis
  Paraneoplastic necrotic
  Perimysial pathology
  Pipestem capillaries
  Scleromyxedema
  Signal recognition particle
  Trichinosis: Acute; Chronic
  Vasculitis: Small & Large vessel

Myopathy: Other
  Atrophy: Type I; Type 2
  CADASIL: Vessels
  Calciphylaxis
  Colchicine
  Cytoplasmic bodies
  Hemosiderin
  Internal architecture: NADH
  Mitochondrial
    Cytochrome oxidase deficiency
    MELAS
    Ultrastructure
  Myosin-loss myopathy
  Posterior neck
  Ring fibers
  Tubular aggregates

Muscle
  Exercise changes
  Unknowns

Muscle: Storage
  Amyloid
    Pathology; Birefringence
  CADASIL
  Carbohydrate
    Acid Maltase Deficiency
      Child & Adult
    Phosphorylase deficiency
    Also see: Pathways
  Lipid
  Lipofuscin
  Myofibrillar (Desmin-storage)

Myopathy: Congenital
  Cap
  Central core
  Centronuclear (Myotubular)
  Congenital muscular dystrophy
  Fiber type size disproportion
    Fiber type disorders
    Type I small
    Type II small
  Fukuyama
  Marinesco-Sjögren
  Multicore
  Nemaline rod myopathy
  Reducing body
  Ullrich CMD

Myopathy: Hereditary
  Autophagy
  Becker MD
  Danon disease
  Distal myopathy: Vacuolar
  Duchenne MD
  Dystrophin & related proteins
  Emery-Dreifuss MD
  FSH Dystrophy
  Hereditary IBM 2
  IBM, Paget's & Dementia
  LGMD 1A
  LGMD 2A
  LGMD 2B
  LGMD 2C
  LGMD 2D
  Myotonic: DM1; DM2
  Oculopharyngeal
  Periodic paralysis, Hypokalemic

Myelin
  CIDP
    Childhood
  Demyelination: Chronic
  Dysmyelination
  Proteins
Neuromuscular junction
  Anti-AChR antibody actions
  Distal motor axons
  Normal
  Myasthenia Gravis
  Terminal axons
  Presynaptic
  Postsynaptic

Neuropathy & Neuronopathy
  Amyloid
  Angiotropic Lymphoma
  Antibody-related
    MAG
    TS-HDS
  Axonal loss
    Bungner bands
    Large fiber
  Axonal swellings
    Giant axonal neuropathy
    Polygucosan bodies
  Botulism
  Demyelination
    Active
    Chronic
    Tomaculae
  Denervation of muscle
    ALS
    Chronic partial denervation
    Fiber type grouping
    Large grouped atrophy
    Ongoing
    Spinal muscular atrophy
        Bulbospinal
        SMA 5q
    Target fibers
  Differential fascicular loss
  Dysmyelination
  Minifascicles
  Nerve: Normal
  Perineuritis
  Regeneration
  Subperineurial edema
  Tabes dorsalis
  Terminal sprouting
  Vasculitis
  Vasculopathy
    Vessel: Thick wall
  Wallerian degeneration

Credits
  All histochemical stains performed by Jim Planer
  Immunocytochemical stains performed by Jin Yue, Shobna Mehta or Rati Choksi


Illustrations

Cell constituents & Pathways
  Acetylcholine receptors
  Botulinum toxin
  Dystrophin & DAGs
  Fatty acid transport
  Glycogen & Glucose metabolism
  Glycolipids
  Ion channels
    Ca++; Na+; K+
  Lysosomal pathway
  Mitochondrial
  Myelin proteins
  Myogenesis
  Neuromuscular junction
  Spliceosome
    Function & Mechanism
  Tendon reflex arcs
  Ubiquitin-Proteasome Pathway
  Vitamins

Muscle fiber
  Excitation-Contraction Coupling
  Myosin & related proteins
  Structure & contraction

Autonomic
  Pathways

Cranial nerve anatomy
  Visual fields
  3, 4, 5, 6, 7, 8, 9, 10, 11, 12

Antibodies
  ANA patterns
  Anti-neural (cerebellum)
Electrophysiology
  Complex repetitive discharges
  Conduction Block: Motor
  Denervation of muscle
    Partial
    Fibrillations
    Motor unit: Rapid firing
  Demyelinating neuropathy
  Myasthenia gravis
  Myasthenic syndrome
  Myokymia
  Myopathy
  Myotonia
  Palmaris brevis spasm
  Positive sharp waves
  Prolonged distal latency
  Pseudofacilitation
  Repetitive response to 1 stimulus
  Stiffman syndrome
  Temporal dispersion
  Tetany

MRI & Imaging
  ALS
  AVM
  Bent spine syndrome
  Calcinosis
  CMT-X1
  Corpus callosum: Thin
  Dystrophinopathy: Female carrier
  Focal myositis
  Hematoma (Psoas)
  HIBM2
  Heroin myelopathy
  Nephrogenic fibrosis
  Posterior neck myopathy
  Superficial siderosis
  Syringomyelia
  Thymoma
Patient pictures
  Acromegaly
  Addison's disease
  Aging
  ALS: MRI; Tongue
  Ankylosing spondylitis
  Becker dystrophy: Legs
  Bethlem myopathy: Hands
  Bulbo-Spinal Muscular Atrophy
  Calcinosis
  Cleidocranial dysplasia
  CMT-X1
  Congenital muscular dystrophy
  Congenital myasthenia gravis
  Duchenne MD
  FSH dystrophy
  Giant axonal neuropathy
  Hereditary sensory neuropathy
  HIBM + Dementia & Pagets
  King-Denborough Syndrome
  Muscle wasting
  Myasthenia gravis
  Myxedema
  Myositis
    Dermatomyositis: Hands; Rash
    Inclusion body myositis
    Pyomyositis (MRI)
  Polio
  SMA 5q: A; B

Disease pathophysiology
  DNA: CTG repeats
  DM1 locus
  FSH DNA
  Myasthenia gravis



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8/19/2009