
FATTY ACID TRANSPORT & OXIDATION
FATTY ACID TRANSPORT
From MW King
- Fatty acids are activated in cytoplasm to Acyl CoA
- Acyl CoA transport through the mitochondrial membranes
- Via acyl carnitine intermediate
- CPT I enzyme in outer mitochondrial membrane
- CPT II enzyme in inner mitochondrial membrane
- Fatty acid-CoA in mitochondria is substrate for
β-oxidation
FATTY ACID OXIDATION
See: Fatty acid oxidation disorders
Return to Mitochondrial pathways
Return to Carnitine disorders
Return to Neuromuscular
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2/3/2001