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![]() Erythema ![]() Gottron's papules ![]() Nailfold lesions From: Chinju, South Korea |
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Antibodies CK: Serum Electrodiagnostic Neoplasm associations Other systemic Pain Pathology Prognosis Skin lesions Treatment Weakness |
Pathological classification of |
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Inflammation Muscle fiber pathology Capillaries Mitochondrial Connective tissue Matrix metalloproteinase MHC-I |
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Subtypes Clinical features Laboratory Treatment |
| Syndrome | Distinctive features |
| Idiopathic | Proximal weakness; High CK; Inflammatory myopathy |
| Collagen vascular disease | Myalgias; Younger onset Scleroderma & Mixed connective tissue disease |
| Anti-t-rna synthetase antibodies Jo-1 antibodies |
Interstitial pneumonitis; Raynauds; Arthritis Perimysial pathology |
| Signal recognition particle antibody | Acute onset;
Severe weakness Capillary pathology; Fibrosis |
| MAS antibody | Acute onset; Rhabdomyolysis |
| Brachio-Cervical | Brachiocervical weakness; B-cell inflammation |
| Drug-induced | D-penicillamine |
| Familial | Homozygosity at HLA-DQA1 locus |
| Graft-vs-host disease | 7 to 24 months post BMT |
| Granulomatous | Sarcoid; Immune; Infections |
| Sarcoidosis | Myopathy; Neuropathy; Lung disease |
| Malignancy (Necrotic) | Rapid onset; Older patients; Necrotic myopathy |
| Mitochondrial (P-COX) | Quadriceps weakness; Older onset age; Steroid resistant |
| Other systemic disorders | HIV; Fasciitis |
![]() Charcot |
![]() Mid-Thoracic
![]() Lower-Thoracic
Interstitial pneumonitis: Jo-1 myositis
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| D-penicillamine |
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MYOSITIS + SKIN CHANGES Dermatomyositis Clinical features Laboratory Pathology Description Histology Treatment Classification Dermatomyositis Childhood Adult Amyopathic Mi-2 antibody negative Malignancy-associated Jo-1 antibody positive EJ antibody positive PM-Scl Childhood & Adult Mi-2 antibody positive |
![]() Tim Miller |
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Absent chondroitin sulfate C Experimental autoimmune myositis Fasciitis Focal myositis Granulomatous Hemophagocytic lymphohistiocytosis Hereditary Infection Necrotizing with pipestem capillaries Orbital Perimyositis |
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General features Neurological features Myopathy Neuropathy Myelopathy Laboratory Pathology Treatment |
![]() Hilar adenopathy
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![]() T1 contrast Multiple lesions in cord & root
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![]() T2 Cord edema
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| MRI: CNS Sarcoid; Myelopathy & Radiculopathy | |
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![]() CDC |
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Other information CDC eMedicine Parasites Georgia User name = guest Password = visitor Ohio State McGill |
![]() From USDA Sarcocystis in muscle
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Eosinophilic fasciitis Chronic skin lesions |