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Stiffman Syndrome & Stimulus sensitive jerking: Neurophysiology

Stiffman syndrome


Stimulus sensitive jerking: Neurophysiology 1
Pattern &
Distribution
Burst
duration
Habituation Muscle
recruitment
order
EEG &
Evoked
potentials
Stiffman
(Spasmodic
  reflex
    myoclonus)
Proximal > Distal
Extensor
General
> 500 ms Prominent & from
Spinal cord entry
Normal
Propriospinal
Myoclonus
Axial
Flexor
General
40 to 140 ms No & from
Spinal cord entry
Normal
Hyperekplexia Proximal > Distal
Flexor
General
20 to 400 ms No & from
11th nerve
± Epileptic EEG
Large SEP
Reticular
Reflex
Myoclonus
Proximal > Distal
Flexor
General
20 to 50 ms No & from
11th nerve
Epileptic EEG
Large SEP
Cortical
Reflex
Myoclonus
Distal > Proximal
Multifocal
20 to 50 ms No from
5th or 7th nerve
Epileptic EEG
Large SEP
Psychogenic
jerks
Inconsistent
General
Variable Yes Variable Normal


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References
1. J Neurol 1995;242:134-142


1/5/2017