Adult pathology Child pathology 1 year 1 month |
![]() H & E stain Storage material in many muscle fibers |
![]() H & E stain |
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Storage & Vacuoles in many muscle fibers
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![]() Gomori trichrome stain |
![]() Gomori trichrome stain |
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NADH-stained membranes are displaced by storage material | |
![]() NADH stain |
![]() NADH stain |
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PAS-stained muscle fibers Diffusely increased staining in fibers |
ATPase stained muscle fibers Remaining intact fibers are mostly type 2 |
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![]() PAS stain |
![]() ATPase pH 9.4 stain |
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Acid phosphatase-stained muscle fibers Increased staining of muscle fiber cytoplasm. Few acid phosphatase positive granules (Right) |
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![]() Acid phosphatase stain |
![]() Acid phosphatase stain |
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![]() Toluidine blue stained plastic sections |
![]() Earlier stage: Most glycogen storage is in membrane bound structures |
![]() Later stage: More glycogen storage is in cytoplasm |
![]() From L Gutmann Acid maltase deficiency: Glycogen deposits (Gray arrows) in smooth muscle cells in vessel walls |
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Cortex![]() |
Motor neurons![]() |
![]() &E stain |
![]() H&E stain |
![]() &E stain |
![]() &E stain |
![]() VvG stain |
![]() NADH stain |
![]() PAS stain |
![]() PAS stain |
![]() H&E stain |
![]() VvG stain |
![]() PAS stain |
![]() PAS stain |