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Brancher Deficiency (GSD 3)

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Images from: Tahseen Mozaffar; Mari Perez-Rosendahl

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H&E stain

Muscle fibers
  Size: Varied
  Contain: Vacuoles, Multiple, Variably-sized

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H&E stain

H&E stain

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PAS stain

PAS: Stains some rounded cytoplasmic aggregates

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Toluidine blue-stained Plastic section

Cytoplasmic Storage: Metachromatic pink color

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GSD3: Muscle Ultrastructure

Glycogen storage
  Deposits: Large, Nonmembrane bound, Sarcoplasmic
  Contents: Glycogen granules, Normal

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Return to GSD3

8/10/2020