Brancher Deficiency (GSD 3)
Images from:
Tahseen Mozaffar;
Mari Perez-Rosendahl
![](../pics/biopsy/muscle/gsd3/gsdhefrozmp.jpg)
H&E stain
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Muscle fibers
Size: Varied
Contain: Vacuoles, Multiple, Variably-sized
![](../pics/biopsy/muscle/gsd3/gsdhefrozhp.jpg)
H&E stain
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![](../pics/biopsy/muscle/gsd3/gsdhefixlongmp.jpg)
H&E stain
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![](../pics/biopsy/muscle/gsd3/gsd3pas.jpg)
PAS stain
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PAS: Stains some rounded cytoplasmic aggregates
![](../pics/biopsy/muscle/gsd3/gsdtbplast.jpg)
Toluidine blue-stained Plastic section
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Cytoplasmic Storage: Metachromatic pink color
GSD3: Muscle Ultrastructure
Glycogen storage
Deposits: Large, Nonmembrane bound, Sarcoplasmic
Contents: Glycogen granules, Normal
Return to
GSD3
8/10/2020